சுருக்கம்

Biliary atresia associated by situs anomalies: 3 case reports.

Ashjaei Bahar*, Mirsharifi Alireza

Biliary atresia is an obliterative process caused by an unknown pathogenesis. Biliary atresia has an estimated incidence of 1/8000 to 1/20000 reported different sources. Hepatoportoentrostomy (Kasai) has been introduced as a choice of biliary atresia treatment which causes long time survival with a native liver and jaundice free clinical state. Biliary atresia can be the cause of cholestatic jaundice in neonates and infants. It can be due to idiopatic, destructive, viral, inflammatory process, ischemic, toxic and remodeling arrest in extrahepatic and intrahepatic bile ducts. Situs inversus is a rare finding in neonates; however biliary atresia is seen to be associated by situs anomalies. Other congenital and gastrointestinal anomalies like malrotation, duodenal atresia, tracheoesophageal fistula and esophageal atresia, biliary atresia were found in 58% of these patients. Here, we present 3 case reports.